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Publications Cytopénies auto-immunes (PTI/AHAI/Evans)

Synergistic convergence of microbiota-specific systemic IgG and secretory IgA

Immune/microbial interface perturbation in human IgA deficiency.

Microbial ecology perturbation in human IgA deficiency.

Campylobacter infection in adult patients with primary antibody deficiency.

Clinical and economic aspects of newborn screening for severe combined immunodeficiency: DEPISTREC study results.

Spectrum of pulmonary aspergillosis in Hyper IgE syndrome with autosomal dominant STAT3 deficiency.

Lymphoproliferative disease in patients with Wiskott-Aldrich syndrome: Analysis of the French Registry of Primary Immunodeficiencies.

The European Society for Immunodeficiencies (ESID) Registry Working Definitions for the Clinical Diagnosis of Inborn Errors of Immunity.

Genetic diagnosis of primary immunodeficiencies: A survey of the French national registry
Progressive Multifocal Leukoencephalopathy in Primary Immunodeficiencies.

Intestinal dysbiosis in inflammatory bowel disease associated with primary immunodeficiency.


Pediatric Evans syndrome is associated with a high frequency of potentially damaging variants in immune genes.

Neurological Involvement in Childhood Evans Syndrome.


Systematic Detection of Portal or Splenic Vein Thrombosis after Splenectomy for Immune Cytopenia.

Risk factors for bleeding, including platelet count threshold, in newly diagnosed immune thrombocytopenia adults.

Pediatric-onset Evans syndrome: Heterogeneous presentation and high frequency of monogenic disorders including LRBA and CTLA4 mutations. 


Treatment with cyclosporin in auto-immune cytopenias in children: The experience from the French cohort OBS’CEREVANCE.

Pathogenesis of immune thrombocytopenia. Audia S et al. Autoimmun Rev. 2017 Jun;16(6):620-632.

Benefits of rituximab as a second-line treatment for autoimmune haemolytic anaemia in children: a prospective French cohort study. Ducassou S et al. Br J Haematol. 2017 Jun;177(5):751-758.

Reliable assessment of the incidence of childhood autoimmune hemolytic anemia. Aladjidi N et al. Pediatr Blood Cancer. 2017 Jul 27.

Evaluation of the efficiency of hydroxychloroquine in treating children with immune thrombocytopenia (ITP). Roche O et al. Am J Hematol. 2017 May;92(5):E79-E81.

A randomized and double-blind controlled trial evaluating the safety and efficacy of rituximab for warm auto-immune hemolytic anemia in adults (the RAIHA study). Michel M et al. Am J Hematol. 2017 Jan;92(1):23-27.

Long-term complications of splenectomy in adult immune thrombocytopenia. Thai LH et al. Medicine (Baltimore). 2016 Nov;95(48):e5098

La plus grande série au monde de syndromes d' Evans chez l'enfant, publiée par le groupe CEREVANCE: Evans Syndrome in Children: Long-Term Outcome in a Prospective French National Observational Cohort. Front Pediatr. 2015 Sep 29;3:79.

Stabilité du nombre de patients adultes hospitalisés pour un PTI chaque année en France : le recours aux IgIV concernent la moitié d’entre eux, le recours au rituximab est stable et le recours à la splénectomie tend à décroître: Management of immune thrombocytopenia in adults: a population-based analysis of the French hospital discharge database from 2009 to 2012. Br J Haematol. 2015 Mar 31.

Vincristine efficacy and safety in treating immune thrombocytopenia: a retrospective study of 35 patients. Eur J Haematol. 2015 May 15.

Rituximab as second-line treatment for adult immune thrombocytopenia (the RITP trial): a multicentre, randomised, double-blind, placebo-controlled trial.
 
Integrated analysis of long-term safety in patients with chronic immune thrombocytopaenia (ITP) treated with the thrombopoietin (TPO) receptor agonist romiplostim.
 
Remission and platelet responses with romiplostim in primary immune thrombocytopenia: final results from a phase 2 study.

Efficacy and safety of the thrombopoietin receptor agonist romiplostim in patients aged ≥ 65 years with immune thrombocytopenia.
 
Cutaneous rash and dapsone-induced hypersensitivity syndrome a common manifestation in adult immune thrombocytopenia. Presentation and outcome in 16 cases.
 
Emergence of long-lived autoreactive plasma cells in the spleen of primary warm auto-immune hemolytic anemia patients treated with rituximab.


 

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